West Virginia Medical Journal - 2024 - Quarter 3 | Page 25

itors have shown some promise in JDM , but evidence is limited to case reports and case studies . 10
Children in the younger age of onset ( 3 years or less ) were found to have milder disease at onset and were more likely to have inactive disease five and 10 years after diagnosis . 7 Juvenile dermatomyositis has a wide variety of presentations and severity , but there is currently no way to predict disease severity . Further research is needed to identify predictors of disease severity to tailor treatment so patients can either receive more intense therapy for more severe cases or less intense therapy for milder cases to minimize side effects from treatment . 10
CONCLUSION
Our case adds to the scant published reports of JDM in younger children , who may not necessarily present in the classic manner . The clinician must keep the diagnosis of JDM in mind in this younger age group (< 3 years old ) whether presenting with all or partial classic findings .
REFERENCES
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2 . Covaci S , Farkas O , Cochino A . Juvenile dermatomyositis . Romanian Journal of Pediatrics . 2016 ; 65 ( 4 ), 373-376 . doi : 10.37897 / RJP . 2016.4.8 .
3 . Papa V , Romanin B , Bergamaschi R et al . Juvenile dermatomyositis : A report of three cases . Ultrastructural Pathology . 2016 ; 40 ( 2 ), 83-5 . doi : 10.310 9 / 01913123.2016.1141823 .
4 . Rego de Figueiredo I , Guerreiro Castro S , Bernardino V , Silva Nunes J , Alves P , Moraes-Fontes M . Juvenile dermatomyositis forty years on : Case report . Neuromuscular Disorders , 2018 ; 28 ( 9 ), 791-797 . doi : 10.1016 / j . nmd . 2018.06.011
5 . Barut K , Aydin PO , Adrovic A , Sahin S , Kasapcopur O . Juvenile dermatomyositis : a tertiary center experience . Clinical Rheumatology . 2017 ; 36 ( 2 ), 361 – 366 . doi : 10.1007 / s10067-016-3530-4 .
6 . Lundberg IE , Tjärnlund A , Bottai M et al . 2017 European league against rheumatism / American college of rheumatology classification criteria for adult and juvenile idiopathic inflammatory myopathies and their major subgroups . Annals of the Rheumatic Diseases . 2017 ; 76 ( 12 ), 1955 – 1964 . doi : 10.1136 / annrheumdis-2017-211468 .
7 . Patwardhan A , Rennebohm R , Dvorchik I , Spencer CH . Is juvenile dermatomyositis a different disease in children up to three years of age at onset than in children above three years at onset ? A retrospective review of 23 years of a single center ' s experience . Pediatr Rheumatol Online J . 2012 Sep 20 ; 10 ( 1 ): 34 . doi : 10.1186 / 1546-0096-10-34 . PMID : 22995763 ; PMCID : PMC3599465 .
8 . Huber AM , Giannini EH , Bowyer SL et al . Protocols for the initial treatment of moderately severe juvenile dermatomyositis : results of a children ' s arthritis and rheumatology research alliance consensus conference . Arthritis Care & Research . 2010 ; 62 ( 2 ), 219 – 25 . doi . org / 10.1002 / acr . 20071 .
9 . Huber AM , Robinson AB , Reed AM et al . Consensus treatments for moderate juvenile dermatomyositis : beyond the first two months . results of the second childhood arthritis and rheumatology research alliance consensus conference . Arthritis Care & Research . 2012 ; 64 ( 4 ), 546 – 53 . doi . org / 10.1002 / acr . 20695 .
10 . McCann LJ , Livermore P , Wilkinson MGL , Wedderburn LR . Juvenile dermatomyositis . Where are we now ? Clin Exp Rheumatol . 2022 Feb ; 40 ( 2 ): 394-403 . doi : 10.55563 / clinexprheumatol / 56ilob . Epub 2022 Feb 7 . PMID : 35225221 .
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