The Journal of the Arkansas Medical Society Issue 2 Vol 115 | Page 13

A C L O S E R Using technology, hearing ability must be provided as close as possible to typical hearing level, if the child is to learn to listen and use spoken language. The child’s family may choose one of five language educa- tion programs: • Auditory-oral: teaches child to use residual hearing by using hear- ing aids or cochlear implants plus speechreading (lip reading); no sign language • Auditory-verbal: includes above plus teaching parents to help child become auditory communicator; no speechreading or sign language • Bilingual-bicultural: teaches child to use American Sign Language (ASL) as first language and English as second; deaf culture is taught with ASL as common language • Cued speech: teaches child how to see and hear spoken language • Total communication: teaches combination of all methods plus ASL Parent involvement is critical to finding the best choice for each child. Language education programs must start by six months to maximize a child’s ability to learn language. (https://www.cdc.gov/ncbddd/hear- ingloss/freematerials/Communica- tion_Brochure.pdf) To accomplish the goal of early intervention by six months, we must: • Screen all babies for hearing loss before one month of age • Ensure that babies who do not pass the screen receive an audiologic evaluation no later than three months (https://www. cdc.gov/ncbddd/hearingloss/ screening.html) • Enroll babies with confirmed hearing loss in early intervention services no later than six months L O O K AT Q U A L I T Y A CLOSER LOOK AT QUALITY A major obstacle to these goals is the delay caused by repeating the failed screening exam after one month of age, before receiving complete audiologic evaluation. Any baby older than one month who h as failed the hearing screen should have an expeditious audiologic evaluation to confirm or rule out hearing loss. This will allow early diagnosis and interven- tion services to begin no later than six months. Delays in early intervention result in permanent spoken language delays. Evidence indicates that many children with sensorineural hearing loss experience improved language abilities with early intervention. Children with hearing loss are at risk not only for lifelong deficits in speech and language acquisition, but poor academic performance, personal- social maladjustments and emotional difficulties. Children with hearing loss are at risk not only for lifelong deficits in speech and language acquisition, but poor academic performance, personal-social maladjustments and emotional difficulties. In addition to developmental delays, these children may have behavioral problems such as attention deficit/hyperactivity disorder, autism or learning disabilities. They should have regular surveillance of developmental milestones. The CDC’s Learn the Sign Act Early (LTSAE) materials and smart phone Milestone app are useful tools to teach parents how to monitor their child’s development. (Free download: www.cdc.gov/MilestoneTracker) Patients may find this simpler tool (https://afmc.org/product-category/ practices/epsdt-well-child-practices/) more helpful. When delays are detected in any domain, the child’s primary care provider (PCP) should do a complete developmental screening with a tool like the Ages and Stages Questionnaire. While virtually all babies born in Arkansas are screened for hearing loss, those who fail the screen are not being diagnosed in a timely man- ner. We are failing to provide early intervention services by six months for all babies diagnosed with hearing loss. Delays are never acceptable. All PCPs, otolaryngologists, audiologists and early intervention providers must work together to be sure that all of Arkansas’ babies with hearing loss get timely, early-intervention services. Hearing loss in babies is a neurodevelopmental emergency. Any delay in auditory stimulation, or a reduced auditory signal during the optimal developmental stage, may cause permanent, irretrievable reassignment of auditory brain cells. There is a limited window of time during which babies can catch up to their normal-hearing peers. s Dr. Mease is Medical Director, Child and Adolescent Health, Arkansas Department of Health. REFERENCES 1. Appler JM and Goodrich LV, Connecting the ear to the brain: Molecular Mecha- nism of Auditory Circuit Assembly, Prog Neurobiol 2011 Apr; 93(4): 488 2. Yoshinaga-Itano, Sedley, Wiggin, Chung, Early Hearing and Vocabulary of Children with Hearing Loss, Pediatrics. 2017; 140(2) 3. American Academy of Pediatrics, Guid- ance for the Clinician in Rendering Pediatric Care, Clinical Report- Hearing Assessment in Infants and Children: Recommendations Beyond Neonatal Screening. Pediatrics. 2009; 124; 1252 NUMBER 2 AUGUST 2018 • 37