Medical Chronicle May 2017 | Page 29

CLINICAL NEUROLOGY PARKINSON’S: AN OVERVIEW There is no cure yet for Parkinson’s disease, but there are numerous therapies that help the symptoms. SYMPTOMS The four basic, so called 'cardinal signs' include tremor, slowness of movement, stiffness of movement Parkinson's disease (PD) is a chronic and progressive movement disorder, meaning that symptoms continue and worsen over time. Nearly one million people in the US are living with Parkinson's disease. The cause is unknown, and although there is presently no cure, there are treatment options such as medication and surgery to manage its symptoms. Parkinson’s disease was first described 200 years ago in 1817 by Dr James Parkinson, a London-based physician. However, the cause of this neurological disease remains elusive. Parkinson's disease may produce a great variety of symptoms, but the four basic, so called 'cardinal signs' include tremor, slowness of movement, stiffness of movement, and impairment of balance. There is no test for Parkinson's disease. Diagnosis is established by listening to the symptoms and physical examination by an experienced clinician. Parkinson’s involves the malfunction and death of neurons. Parkinson's primarily affects neurons in the substantia nigra. Some of these dying neurons produce dopamine, which sends messages to the part of the brain that controls movement and coordination. As PD progresses, the amount of dopamine produced in the brain decreases, leaving a person unable to control movement normally. The specific group of symptoms that an individual experiences varies from person to person. Primary motor signs of PD include the following. • Tremour of the hands, arms, legs, jaw and face • Bradykinesia or slowness of movement • Rigidity or stiffness of the limbs and trunk • Postural instability or impaired balance and coordination. Scientists are also exploring the idea that loss of cells in other areas of the brain and body contribute to Parkinson’s. For example, researchers have discovered that the hallmark sign of Parkinson’s disease - clumps of a protein alpha-synuclein, which are also called Lewy Bodies - are found not only in the mid-brain but also in the brain stem and the olfactory bulb. These areas of the brain correlate to nonmotor functions such as sense of smell and sleep regulation. The presence of Lewy bodies in these areas could explain the nonmotor symptoms experienced by some people with PD before any motor sign of the disease appears. The intestines also have dopamine cells that degenerate in Parkinson’s, and this may be important in the gastrointestinal symptoms that are part of the disease. The four primary symptoms of Parkinson’s are tremour or trembling in hands, arms, legs, jaw, and face; rigidity or stiffness of the limbs and trunk; bradykinesia, or slowness of movement and postural instability or impaired balance and coordination. Patients may also have difficulty walking, talking, or completing other simple tasks. The disease is both chronic and progressive. Parkinson’s is not usually inherited. Early symptoms are subtle and occur gradually. Dyskinesia is usually lifelong and progressive; therefore, physicians generally see the disorder in elderly patients. Medical treatment must be carefully selected on the basis of the cause of the dyskinesia. Parki nsonian dyskinesia is well controlled by drug therapy. However, patients can become less responsive to a drug after years of use and may experience unwelcome side effects. Cerebellar tremor is extremely disabling because it worsens with activity, but no satisfactory therapy is available. Senile, essential, and familial tremours are also intensified by action, but they can often be suppressed with a mild tranquiliser or a beta blocker. Drug treatment of blepharospasm and spastic dysphonia has been disappointing: Facial or laryngeal surgery is sometimes required. Tardive dyskinesia is caused by neuroleptic drugs, so the only therapy for the disorder is withdrawal of the offending drug. TREATMENT A variety of medications provide dramatic relief from the symptoms, but no drug can stop the progression of the disease. In some cases, surgery is an appropriate treatment. Some doctors recommend physical therapy or muscle-strengthening exercises. References available on request. S4 Biperiden Hydrochloride (Each Tablet Contains 2mg Biperidin Hydrochloride) Recommended dosage for the treatment of Parkinson's Disease B1042 (Act 101/1965) Reference: 1. MCC approved package insert. 2. Carr J. Guideline for the treatment of Parkinson’s disease SAMJ 2009. REF1702AKIAD01 MEDICAL CHRONICLE | MAY 2017 29