July/August 2017 | Page 35

Discussion B. Melanotic macules (MM) are benign, pigmented lesions that clinically present as brown, flat discolorations of the oral mucosa, representing 86.1% of melanocytic lesions of the lips and oral cavity (Figure 4). 4, 5 The discoloration is caused by a focal increase in melanin deposition with or without a concomitant increase in the number of melanocytes. The cause is unknown, but it does not appear to be dependent on sun exposure. This differs from the common cutaneous freckle, or ephelis, which darkens in color with sun exposure. However, it is hypothesized that MMs present on the vermilion border may be related to actinic irradiation (Figure 5). 2 Clinically, the lesion presents over a wide age range, with an average age of 43 years, and a 2:1 female predilection. 4 MMs appear as asymptomatic, solitary, well-demarcated, tan to dark-brown, flat lesions in 83% of cases. 2 The color is uniform throughout the lesion. Patients occasionally present with multiple macular lesions. Additionally, blue or black lesions have also been reported. The most common locations are on the lower lip at the vermilion border, followed by the buccal mucosa, gingiva (commonly the maxillary anterior gingiva), and palate. 2, 4 MMs reach their maximum dimension rapidly and remain constant thereafter. Histologically, the lesion displays an increase in melanin pigmentation in the basal and parabasal layers of normal, stratified squamous epithelium, without elongated rete ridges. Melanin incontinence (free melanin) may be seen in the subjacent connective tissue. While MM was considered in the differential diagnosis in this case, the presence of foreign material, the staining of the reticulin fibers, and the absence of basal and parabasal melanin ruled out this entity. Figure 5 A flat, round, uniformly pigmented melanotic macule of the lower left lip. MM is a benign entity with no potential for malignant transformation. However, they are important for two reasons: 1) they may be an oral manifestation of a systemic condition and 2) early oral mucosal melanoma can appear similar clinically. In addition to an idiopathic cause, cases of multiple, pigmented, flat lesions may be associated with systemic conditions (e.g., Peutz-Jeghers syndrome, McCune-Albright syndrome, Addison disease) or certain medications or irritants can increase melanin pigmentation (e